Robinson, Hannah, Deykin, Alexey V., Bronovitsky, Evgeny V., Ovchinnikov, Ruslan K., Ustyugov, Alexey A., Shelkovnikova, Tatyana ORCID: https://orcid.org/0000-0003-1367-5309, Kukharsky, Michail S., Ermolkevich, Tatyana G., Goldman, Igor L., Sadchikova, Elena R., Kovrazhkina, Elena A., Bachurin, Sergey O., Buchman, Vladimir L. ORCID: https://orcid.org/0000-0002-7631-8352 and Ninkina, Natalia ORCID: https://orcid.org/0000-0001-8570-5648 2015. Early lethality and neuronal proteinopathy in mice expressing cytoplasm-targeted FUS that lacks the RNA recognition motif. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 16 (5-6) , pp. 402-409. 10.3109/21678421.2015.1040994 |
Robinson, Hannah
2015.
Structural modifications of the RNA-binding protein, fused in sarcoma: implications for amyotrophic lateral sclerosis.
PhD Thesis,
Cardiff University.
Item availability restricted. |
Shelkovnikova, Tatyana A. ORCID: https://orcid.org/0000-0003-1367-5309, Robinson, Hannah K., Southcombe, Joshua A., Ninkina, Natalia ORCID: https://orcid.org/0000-0001-8570-5648 and Buchman, Vladimir L. ORCID: https://orcid.org/0000-0002-7631-8352 2014. Multistep process of FUS aggregation in the cell cytoplasm involves RNA-dependent and RNA-independent mechanisms. Human Molecular Genetics 23 (19) , pp. 5211-5226. 10.1093/hmg/ddu243 |
Shelkovnikova, Tatyana ORCID: https://orcid.org/0000-0003-1367-5309, Robinson, Hannah, Troakes, C., Ninkina, Natalia ORCID: https://orcid.org/0000-0001-8570-5648 and Buchman, Vladimir ORCID: https://orcid.org/0000-0002-7631-8352 2014. Compromised paraspeckle formation as a pathogenic factor in FUSopathies. Human Molecular Genetics 23 (9) , pp. 2298-2312. 10.1093/hmg/ddt622 |
Shelkovnikova, Tatyana ORCID: https://orcid.org/0000-0003-1367-5309, Peters, Owen Morgan ORCID: https://orcid.org/0000-0002-6824-0663, Deykin, Alexey V., Connor-Robson, Natalie ORCID: https://orcid.org/0000-0001-8350-6928, Robinson, Hannah, Ustyugov, Aleksey ORCID: https://orcid.org/0000-0003-1977-4797, Bachurin, Sergey O., Ermolkevich, Tatyana G., Goldman, Igor L., Sadchikova, Elena R., Kovrazhkina, Elena A., Skvortsova, Veronica I., Ling, Shuo-Chien, Da Cruz, Sandrine, Parone, Philippe A., Buchman, Vladimir L. ORCID: https://orcid.org/0000-0002-7631-8352 and Ninkina, Natalia ORCID: https://orcid.org/0000-0001-8570-5648 2013. Fused in sarcoma (FUS) protein lacking nuclear localization signal (NLS) and major RNA binding motifs triggers proteinopathy and severe motor phenotype in transgenic mice. Journal of Biological Chemistry 288 (35) , pp. 25266-25274. 10.1074/jbc.M113.492017 |